An Unusual Case of Incontinentia Pigmenti Presenting with Papules and Plaques
نویسندگان
چکیده
Incontinentia Pigmenti, also known as Bloch-Sulzberger syndrome, is a rare X-linked dominant disorder considered to be lethal in males. The syndrome usually presents at birth or shortly thereafter and the skin rash evolves in the classic four stages of vesicular, verrucous, hyperpigmented, and hypopigmented lesions following a blaschko linear distribution. Here we present an unusual case of Incontinentia Pigmenti presenting with papules and plaques preceding the classic evolution of eruptions.
منابع مشابه
Pruritic urticarial papules and plaques of pregnancy with Bullae formation: Report of an unusual case
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